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Table 1 Likelihood of a typical clinical presentation of dementia with Lewy bodies

From: Neuropathology and molecular diagnosis of Synucleinopathies

Lewy-related pathology

ADNC based on NIA-AA

None/low

Intermediate

High

Diffuse neocortical

High

High

Intermediate

Limbic (transitional)

High

Intermediate

Low

Brainstem-predominant

Low

Low

Low

Amygdala-predominant

Low

Low

Low

Olfactory bulb only

Low

Low

Low

  1. Abbreviations: ADNC Alzheimer’s disease neuropathological change, NIA-AA National Institute on Aging–Alzheimer’s Association guidelines for the neuropathologic assessment of Alzheimer disease